Mouse peroxisomal biogenesis factor 13 ELISA Kit | PEX13 elisa kit
Mouse Peroxisomal membrane protein PEX13, PEX13 ELISA Kit
NCBI and Uniprot Product Information
Uniprot Description
PEX13: Component of the peroxisomal translocation machinery with PEX14 and PEX17. Functions as a docking factor for the predominantly cytoplasmic PTS1 receptor (PAS10/PEX5). Involved in the import of PTS1 and PTS2 proteins. Defects in PEX13 are the cause of peroxisome biogenesis disorder complementation group 13 (PBD-CG13); also known as PBD-CGH. PBD-CG13 is a peroxisomal disorder arising from a failure of protein import into the peroxisomal membrane or matrix. The peroxisome biogenesis disorders (PBD group) are genetically heterogeneous with at least 14 distinct genetic groups as concluded from complementation studies. Include disorders are: Zellweger syndrome (ZWS), neonatal adrenoleukodystrophy (NALD), infantile Refsum disease (IRD), and classical rhizomelic chondrodysplasia punctata (RCDP). ZWS, NALD and IRD are distinct from RCDP and constitute a clinical continuum of overlapping phenotypes known as the Zellweger spectrum (PBD-ZSS). Defects in PEX13 are a cause of adrenoleukodystrophy neonatal (NALD). NALD is a peroxisome biogenesis disorder (PBD) characterized by the accumulation of very long- chain fatty acids, adrenal insufficiency and mental retardation. Belongs to the peroxin-13 family.
Protein type: Membrane protein, integral
Cellular Component: peroxisomal membrane; integral to peroxisomal membrane; intracellular membrane-bound organelle; membrane; integral to membrane; peroxisome
Molecular Function: peroxisome targeting sequence binding
Biological Process: protein transport; cerebral cortex cell migration; suckling behavior; transport; microtubule-based peroxisome localization; neuron migration; protein import into peroxisome matrix, docking; locomotory behavior; fatty acid alpha-oxidation
Research Articles on PEX13
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Product Notes
The Mouse PEX13 pex13 (Catalog #AAA9320161) is an ELISA Kit and is intended for research purposes only. The product is available for immediate purchase. The AAA9320161 ELISA Kit recognizes Mouse PEX13. It is sometimes possible for the material contained within the vial of "peroxisomal biogenesis factor 13, ELISA Kit" to become dispersed throughout the inside of the vial, particularly around the seal of said vial, during shipment and storage. We always suggest centrifuging these vials to consolidate all of the liquid away from the lid and to the bottom of the vial prior to opening. Please be advised that certain products may require dry ice for shipping and that, if this is the case, an additional dry ice fee may also be required.Precautions
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