Western Blot (WB)
(All lanes: Trimethyllysine dioxygenase, mitochondrial antibody at 2ug/ml+MCF-7 the whole cell lysate)
Rabbit anti-Human Trimethyllysine dioxygenase Polyclonal Antibody | anti-TMLHE antibody
Trimethyllysine dioxygenase, mitochondrial Polyclonal Antibody
Western Blot (WB)
(All lanes: Trimethyllysine dioxygenase, mitochondrial antibody at 2ug/ml+MCF-7 the whole cell lysate)
Western Blot (WB)
(All lanes: Trimethyllysine dioxygenase, mitochondrial antibody at 2ug/ml+MCF-7 the whole cell lysate)
NCBI and Uniprot Product Information
Uniprot Description
TMLHE: Converts trimethyllysine (TML) into hydroxytrimethyllysine (HTML). Defects in TMLHE are the cause of epsilon-trimethyllysine hydroxylase deficiency (TMLHED). An inborn error of carnitine biosynthesis associated with an increased risk for developing autistic behavior. Autism is a complex multifactorial, pervasive developmental disorder characterized by impairments in reciprocal social interaction and communication, restricted and stereotyped patterns of interests and activities, and the presence of developmental abnormalities by 3 years of age. Most individuals with autism also manifest moderate mental retardation. Belongs to the gamma-BBH/TMLD family. 8 isoforms of the human protein are produced by alternative promoter.
Protein type: Amino Acid Metabolism - lysine degradation; EC 1.14.11.8; Mitochondrial; Oxidoreductase
Chromosomal Location of Human Ortholog: Xq28
Cellular Component: mitochondrial matrix; mitochondrion
Molecular Function: trimethyllysine dioxygenase activity
Biological Process: carnitine biosynthetic process
Disease: Epsilon-trimethyllysine Hydroxylase Deficiency
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Product Notes
The TMLHE tmlhe (Catalog #AAA9415174) is an Antibody produced from Rabbit and is intended for research purposes only. The product is available for immediate purchase. The Trimethyllysine dioxygenase, mitochondrial Polyclonal Antibody reacts with Human and may cross-react with other species as described in the data sheet. AAA Biotech's Trimethyllysine dioxygenase can be used in a range of immunoassay formats including, but not limited to, Western Blot (WB). Western Blot: 1:500 - 1:1000. Researchers should empirically determine the suitability of the TMLHE tmlhe for an application not listed in the data sheet. Researchers commonly develop new applications and it is an integral, important part of the investigative research process. It is sometimes possible for the material contained within the vial of "Trimethyllysine dioxygenase, Polyclonal Antibody" to become dispersed throughout the inside of the vial, particularly around the seal of said vial, during shipment and storage. We always suggest centrifuging these vials to consolidate all of the liquid away from the lid and to the bottom of the vial prior to opening. Please be advised that certain products may require dry ice for shipping and that, if this is the case, an additional dry ice fee may also be required.Precautions
All products in the AAA Biotech catalog are strictly for research-use only, and are absolutely not suitable for use in any sort of medical, therapeutic, prophylactic, in-vivo, or diagnostic capacity. By purchasing a product from AAA Biotech, you are explicitly certifying that said products will be properly tested and used in line with industry standard. AAA Biotech and its authorized distribution partners reserve the right to refuse to fulfill any order if we have any indication that a purchaser may be intending to use a product outside of our accepted criteria.Disclaimer
Though we do strive to guarantee the information represented in this datasheet, AAA Biotech cannot be held responsible for any oversights or imprecisions. AAA Biotech reserves the right to adjust any aspect of this datasheet at any time and without notice. It is the responsibility of the customer to inform AAA Biotech of any product performance issues observed or experienced within 30 days of receipt of said product. To see additional details on this or any of our other policies, please see our Terms & Conditions page.Item has been added to Shopping Cart
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