Rabbit GBE1 Polyclonal Antibody | anti-GBE1 antibody
GBE1
Gene Names
GBE1; GBE; APBD; GSD4
Reactivity
HumanPredicted: Rat, Mouse
Applications
ELISA, Western Blot, Immunohistochemistry
Purity
Purified By Antigen Affinity Column
Synonyms
GBE1; Polyclonal Antibody; GBE; APBD; GSD4; anti-GBE1 antibody
Host
Rabbit
Reactivity
Human
Predicted: Rat, Mouse
Predicted: Rat, Mouse
Clonality
Polyclonal
Isotype
IgG
Purity/Purification
Purified By Antigen Affinity Column
Form/Format
Already dissolved in sterile H2O with 1% BSA and 0.02% NaN3 and 50% Glycerol.
Sequence Length
2891
Applicable Applications for anti-GBE1 antibody
ELISA (EIA), Western Blot (WB), Immunohistochemistry (IHC)
Application Notes
ELISA: 1:20,000-80,000
WB: 1:200-1,000
IHC: 1:100-500
WB: 1:200-1,000
IHC: 1:100-500
Immunogen
Recombinant fragment corresponding to 386aa-535aa of human GBE1.
Cellular Localization
Cytosol, Extracellular Exosome
Related Product Information for anti-GBE1 antibody
Homo sapiens glucan (1,4-alpha-), branching enzyme 1 (GBE1), mRNA.
References
Paradas C, Akman HO, Ionete C, et al. Branching enzyme deficiency):expanding the clinical spectrum. JAMA Neurol 71(1):41-47 (2014)
NCBI and Uniprot Product Information
NCBI GI #
NCBI GeneID
Molecular Weight
75kd
NCBI Official Full Name
Homo sapiens glucan (1,4-alpha-), branching enzyme 1, mRNA
NCBI Official Synonym Full Names
1,4-alpha-glucan branching enzyme 1
NCBI Official Symbol
GBE1
NCBI Official Synonym Symbols
GBE; APBD; GSD4
NCBI Protein Information
1,4-alpha-glucan-branching enzyme
Protein Family
NCBI Description
The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease). [provided by RefSeq, Jul 2008]
Research Articles on GBE1
Similar Products
Product Notes
The GBE1 (Catalog #AAA8561919) is an Antibody produced from Rabbit and is intended for research purposes only. The product is available for immediate purchase. The GBE1 reacts with Human Predicted: Rat, Mouse and may cross-react with other species as described in the data sheet. AAA Biotech's GBE1 can be used in a range of immunoassay formats including, but not limited to, ELISA (EIA), Western Blot (WB), Immunohistochemistry (IHC). ELISA: 1:20,000-80,000 WB: 1:200-1,000 IHC: 1:100-500. Researchers should empirically determine the suitability of the GBE1 for an application not listed in the data sheet. Researchers commonly develop new applications and it is an integral, important part of the investigative research process. It is sometimes possible for the material contained within the vial of "GBE1, Polyclonal Antibody" to become dispersed throughout the inside of the vial, particularly around the seal of said vial, during shipment and storage. We always suggest centrifuging these vials to consolidate all of the liquid away from the lid and to the bottom of the vial prior to opening. Please be advised that certain products may require dry ice for shipping and that, if this is the case, an additional dry ice fee may also be required.Precautions
All products in the AAA Biotech catalog are strictly for research-use only, and are absolutely not suitable for use in any sort of medical, therapeutic, prophylactic, in-vivo, or diagnostic capacity. By purchasing a product from AAA Biotech, you are explicitly certifying that said products will be properly tested and used in line with industry standard. AAA Biotech and its authorized distribution partners reserve the right to refuse to fulfill any order if we have any indication that a purchaser may be intending to use a product outside of our accepted criteria.Disclaimer
Though we do strive to guarantee the information represented in this datasheet, AAA Biotech cannot be held responsible for any oversights or imprecisions. AAA Biotech reserves the right to adjust any aspect of this datasheet at any time and without notice. It is the responsibility of the customer to inform AAA Biotech of any product performance issues observed or experienced within 30 days of receipt of said product. To see additional details on this or any of our other policies, please see our Terms & Conditions page.Item has been added to Shopping Cart
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