Typical Testing Data/Standard Curve (for reference only)
Mouse Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex ELISA Kit | Dbt elisa kit
Mouse Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial ELISA Kit
Typical Testing Data/Standard Curve (for reference only)
Typical Testing Data/Standard Curve (for reference only)
NCBI and Uniprot Product Information
Uniprot Description
DBT: The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). Defects in DBT are the cause of maple syrup urine disease type 2 (MSUD2). MSUD is an autosomal recessive disorder characterized by mental and physical retardation, feeding problems, and a maple syrup odor to the urine. Belongs to the 2-oxoacid dehydrogenase family.
Protein type: EC 2.3.1.168; Amino Acid Metabolism - valine, leucine and isoleucine degradation; Mitochondrial; Transferase
Cellular Component: mitochondrion
Molecular Function: dihydrolipoyllysine-residue (2-methylpropanoyl)transferase activity; transferase activity; transferase activity, transferring acyl groups; ubiquitin protein ligase binding
Biological Process: metabolic process
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Product Notes
The Mouse Dbt dbt (Catalog #AAA2881204) is an ELISA Kit and is intended for research purposes only. The product is available for immediate purchase. The AAA2881204 ELISA Kit recognizes Mouse Dbt. It is sometimes possible for the material contained within the vial of "Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, ELISA Kit" to become dispersed throughout the inside of the vial, particularly around the seal of said vial, during shipment and storage. We always suggest centrifuging these vials to consolidate all of the liquid away from the lid and to the bottom of the vial prior to opening. Please be advised that certain products may require dry ice for shipping and that, if this is the case, an additional dry ice fee may also be required.Precautions
All products in the AAA Biotech catalog are strictly for research-use only, and are absolutely not suitable for use in any sort of medical, therapeutic, prophylactic, in-vivo, or diagnostic capacity. By purchasing a product from AAA Biotech, you are explicitly certifying that said products will be properly tested and used in line with industry standard. AAA Biotech and its authorized distribution partners reserve the right to refuse to fulfill any order if we have any indication that a purchaser may be intending to use a product outside of our accepted criteria.Disclaimer
Though we do strive to guarantee the information represented in this datasheet, AAA Biotech cannot be held responsible for any oversights or imprecisions. AAA Biotech reserves the right to adjust any aspect of this datasheet at any time and without notice. It is the responsibility of the customer to inform AAA Biotech of any product performance issues observed or experienced within 30 days of receipt of said product. To see additional details on this or any of our other policies, please see our Terms & Conditions page.Item has been added to Shopping Cart
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