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Mouse glycine cleavage system protein H (aminomethyl carrier) ELISA Kit | GCSH elisa kit

Mouse Glycine cleavage system H protein, mitochondrial, GCSH ELISA Kit

Gene Names
Gcsh; 1100001L02Rik; 5730591C18Rik
Reactivity
Mouse
Synonyms
glycine cleavage system protein H (aminomethyl carrier); Mouse Glycine cleavage system H protein; mitochondrial; GCSH ELISA Kit; mitochondrial (GCSH) ELISA kit; GCE; NKH; lipoic acid-containing protein; mitochondrial glycine cleavage system H-protein; part of mitochondrial matrix glycine cleavage enzyme complex of 4 proteins: H-; L-; P-; and T-proteins; GCSH elisa kit
Ordering
For Research Use Only!
Reactivity
Mouse
Preparation and Storage
Store all reagents at 2-8 degree C

NCBI and Uniprot Product Information

NCBI GI #
NCBI GeneID
NCBI Accession #
NCBI GenBank Nucleotide #
UniProt Accession #
Molecular Weight
18,637 Da
NCBI Official Full Name
glycine cleavage system H protein, mitochondrial
NCBI Official Synonym Full Names
glycine cleavage system protein H (aminomethyl carrier)
NCBI Official Symbol
Gcsh
NCBI Official Synonym Symbols
1100001L02Rik; 5730591C18Rik
NCBI Protein Information
glycine cleavage system H protein, mitochondrial; lipoic acid-containing protein
UniProt Protein Name
Glycine cleavage system H protein, mitochondrial
UniProt Gene Name
Gcsh
UniProt Entry Name
GCSH_MOUSE

Uniprot Description

GCSH: The glycine cleavage system catalyzes the degradation of glycine. The H protein shuttles the methylamine group of glycine from the P protein to the T protein. Defects in GCSH are a cause of non-ketotic hyperglycinemia (NKH); also known as glycine encephalopathy (GCE). NKH is an autosomal recessive disease characterized by accumulation of a large amount of glycine in body fluid and by severe neurological symptoms. Belongs to the GcvH family.

Cellular Component: mitochondrion; glycine cleavage complex

Molecular Function: enzyme binding; aminomethyltransferase activity

Biological Process: methylation; glycine decarboxylation via glycine cleavage system

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Product Notes

The Mouse GCSH gcsh (Catalog #AAA9336063) is an ELISA Kit and is intended for research purposes only. The product is available for immediate purchase. The AAA9336063 ELISA Kit recognizes Mouse GCSH. It is sometimes possible for the material contained within the vial of "glycine cleavage system protein H (aminomethyl carrier), ELISA Kit" to become dispersed throughout the inside of the vial, particularly around the seal of said vial, during shipment and storage. We always suggest centrifuging these vials to consolidate all of the liquid away from the lid and to the bottom of the vial prior to opening. Please be advised that certain products may require dry ice for shipping and that, if this is the case, an additional dry ice fee may also be required.

Precautions

All products in the AAA Biotech catalog are strictly for research-use only, and are absolutely not suitable for use in any sort of medical, therapeutic, prophylactic, in-vivo, or diagnostic capacity. By purchasing a product from AAA Biotech, you are explicitly certifying that said products will be properly tested and used in line with industry standard. AAA Biotech and its authorized distribution partners reserve the right to refuse to fulfill any order if we have any indication that a purchaser may be intending to use a product outside of our accepted criteria.

Disclaimer

Though we do strive to guarantee the information represented in this datasheet, AAA Biotech cannot be held responsible for any oversights or imprecisions. AAA Biotech reserves the right to adjust any aspect of this datasheet at any time and without notice. It is the responsibility of the customer to inform AAA Biotech of any product performance issues observed or experienced within 30 days of receipt of said product. To see additional details on this or any of our other policies, please see our Terms & Conditions page.

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