Human enoyl Coenzyme A hydratase, short chain, 1, mitochondrial ELISA Kit | ECHS1 elisa kit
Human Enoyl-CoA hydratase, mitochondrial, ECHS1 ELISA Kit
NCBI and Uniprot Product Information
NCBI Description
The protein encoded by this gene functions in the second step of the mitochondrial fatty acid beta-oxidation pathway. It catalyzes the hydration of 2-trans-enoyl-coenzyme A (CoA) intermediates to L-3-hydroxyacyl-CoAs. The gene product is a member of the hydratase/isomerase superfamily. It localizes to the mitochondrial matrix. Transcript variants utilizing alternative transcription initiation sites have been described in the literature. [provided by RefSeq, Jul 2008]
Uniprot Description
ECHS1: Straight-chain enoyl-CoA thioesters from C4 up to at least C16 are processed, although with decreasing catalytic rate. Belongs to the enoyl-CoA hydratase/isomerase family.
Protein type: Carbohydrate Metabolism - propanoate; Lyase; EC 4.2.1.17; Lipid Metabolism - fatty acid; Carbohydrate Metabolism - butanoate; Amino Acid Metabolism - lysine degradation; Lipid Metabolism - fatty acid elongation in mitochondria; Other Amino Acids Metabolism - beta-alanine; Mitochondrial; Secondary Metabolites Metabolism - limonene and pinene degradation; Amino Acid Metabolism - valine, leucine and isoleucine degradation; Amino Acid Metabolism - tryptophan
Chromosomal Location of Human Ortholog: 10q26.2-q26.3
Cellular Component: mitochondrion; mitochondrial matrix
Molecular Function: protein binding; enoyl-CoA hydratase activity
Biological Process: fatty acid beta-oxidation; cellular lipid metabolic process
Disease: Mitochondrial Short-chain Enoyl-coa Hydratase 1 Deficiency
Research Articles on ECHS1
Similar Products
Product Notes
The Human ECHS1 echs1 (Catalog #AAA9319744) is an ELISA Kit and is intended for research purposes only. The product is available for immediate purchase. The AAA9319744 ELISA Kit recognizes Human ECHS1. It is sometimes possible for the material contained within the vial of "enoyl Coenzyme A hydratase, short chain, 1, mitochondrial, ELISA Kit" to become dispersed throughout the inside of the vial, particularly around the seal of said vial, during shipment and storage. We always suggest centrifuging these vials to consolidate all of the liquid away from the lid and to the bottom of the vial prior to opening. Please be advised that certain products may require dry ice for shipping and that, if this is the case, an additional dry ice fee may also be required.Precautions
All products in the AAA Biotech catalog are strictly for research-use only, and are absolutely not suitable for use in any sort of medical, therapeutic, prophylactic, in-vivo, or diagnostic capacity. By purchasing a product from AAA Biotech, you are explicitly certifying that said products will be properly tested and used in line with industry standard. AAA Biotech and its authorized distribution partners reserve the right to refuse to fulfill any order if we have any indication that a purchaser may be intending to use a product outside of our accepted criteria.Disclaimer
Though we do strive to guarantee the information represented in this datasheet, AAA Biotech cannot be held responsible for any oversights or imprecisions. AAA Biotech reserves the right to adjust any aspect of this datasheet at any time and without notice. It is the responsibility of the customer to inform AAA Biotech of any product performance issues observed or experienced within 30 days of receipt of said product. To see additional details on this or any of our other policies, please see our Terms & Conditions page.Item has been added to Shopping Cart
If you are ready to order, navigate to Shopping Cart and get ready to checkout.
